Pachydermoperiostosis
Pachydermoperiostosis Causes
PDP is often considered as familial in nature, which means it is an inherited condition believed to be autonomic dominant. PDP can also be brought about by other underlying medical conditions such as myelofibrosis, compressive neuropathy, psoriatric onychopathy and gynecomastia as well as congenital cardiac disease.
Pachydermoperiostosis Definition
Pachydermoperiostosis is categorized as a rare disorder that is primarily characterized by clubbing of the fingers, excessive sweating and thickening of the skin of the face. It medical condition typically appears during early childhood or adolescence, and progresses slowly within the next ten year or so.
Pachydermoperiostosis Diagnosis
This disease is diagnosed using radiographs conducted on the long bones, which may reveal some subperiosteal new bone formation. Other radiographic abnormalities can also include cortical thickening and paranasal sinuses.
Pachydermoperiostosis Symptoms and Signs
Specific symptoms of Pachydermoperiostosis include the enlargement of the patient's fingers and toes. This condition features fibrous covering present on the ends of the long bones, and often accompanied with coarse facial features as well as an increased mass of the skin development on the scalp that results to the formation of folds, furrows and depressions.
Pachydermoperiostosis Treatment
Treatment are primarily administered to alleviate this medical condition. Cortisteroids and Nonsteroidal anti-inflammatory drugs are among the common medications. Surgery may also be required in severe cases in the form of a vagotomy that is designed to improve swelling and articular pain. Other patients may also undergo cosmetic surgery.